Autoimmune Autonomic Ganglionopathy (AAG): extremely rare form of dysautonomia in which the body's own immune system damages a receptor in the autonomic ganglia; s/s include severe orthostatic hypotension, syncope, GI dysmotility, urinary retention, fixed & dilated pupils, & dry mouth/eyes. Onset can be acute, subacute, or gradual. No definitive Tx exists, but it is often treated using total plasmapheresis, IVIG, &/or immunosuppressants. Immune System, Autoimmune Disease, Dysautonomia, Neuropathy, Autoimmune Disorder, Syndrome, Disease, Lyme Disease, Disorders
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Autoimmune Autonomic Ganglionopathy Summary

Autoimmune Autonomic Ganglionopathy (AAG) is a very rare form of dysautonomia in which the bodies own immune system damages a receptor in the autonomic ganglia (part of the peripheral autonomic nerve fiber). It is often associated with high titers of ganglionic acetylcholine receptor antibody (g-AChR antibody). AAG can impact people of all ages and both sexes. Approximately 100 Americans are diagnosed with AAG per year. AAG is a treatable antibody-mediated disorder of autonomic ganglionic…

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